Congenital malformations of genital organs (Q50-Q56)
Q56: Indeterminate sex and pseudohermaphroditism

excludes1
46,XX true hermaphrodite (Q99.1)
androgen insensitivity syndrome (E34.5-)
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
female pseudohermaphroditism with adrenocortical disorder (E25.-)
pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
pure gonadal dysgenesis (Q99.1)
Q56.0: Hermaphroditism, not elsewhere classified
Q56.1: Male pseudohermaphroditism, not elsewhere classified
Q56.2: Female pseudohermaphroditism, not elsewhere classified
Q56.3: Pseudohermaphroditism, unspecified
Q56.4: Indeterminate sex, unspecified

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