D57.4: Sickle-cell thalassemia
D57.43: Sickle-cell thalassemia beta zero with crisis

inclusionTerm
HbS-beta zero with crisis
Sickle-cell beta zero with crisis

inclusionTerm
HbS-beta zero with acute chest syndrome
Sickle-cell beta zero with acute chest syndrome

inclusionTerm
HbS-beta zero with splenic sequestration
Sickle-cell beta zero with splenic sequestration

inclusionTerm
HbS-beta zero with cerebral vascular involvement
Sickle-cell beta zero with cerebral vascular involvement

codeAlso
, if applicable cerebral infarction (I63.-)

inclusionTerm
HbS-beta zero with other specified complication
Sickle-cell beta zero with other specified complication

useAdditionalCode
code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)

inclusionTerm
HbS-beta zero with other specified complication
Sickle-cell beta zero with crisis unspecified
Sickle-cell thalassemia beta zero with (painful) crisis NOS
Sickle-cell thalassemia beta zero with vasoocclusive pain NOS
D57.431: Sickle-cell thalassemia beta zero with acute chest syndrome
D57.432: Sickle-cell thalassemia beta zero with splenic sequestration
D57.433: Sickle-cell thalassemia beta zero with cerebral vascular involvement
D57.438: Sickle-cell thalassemia beta zero with crisis with other specified complication
D57.439: Sickle-cell thalassemia beta zero with crisis, unspecified

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